Normalization of Pulmonary Vascular Resistance Long After Successful Primary Sutureless Repair for Congenital Pulmonary Vein Stenosis
- نوع فایل : کتاب
- زبان : انگلیسی
- مؤلف : Takaya Hoashi • Koji Kagisaki • Heima Sakaguchi • Hajime Ichikawa
- چاپ و سال / کشور: 2011
Description
A 3-month-old infant with perimembranous ventricular septal defect (VSD) and pulmonary hypertension presented at our center. Cardiac catheterization showed a systolic pulmonary-to-systemic arterial pressure ratio of 0.99 and a pulmonary vascular resistance of 9.32 lm2. Pulmonary angiography showed focal orifice stenosis in the right lower and left lower and upper pulmonary veins, whereas the right upper pulmonary vein was atretic. Sutureless pericardial marsupialization concomitant with VSD patch closure was used to repair the three stenotic veins. Administration of home oxygen therapy and sildenafil citrate was continued after surgical repair. Postoperative catheterization 1.5 years after surgery showed patency of the three repaired veins and normalization of pulmonary vascular resistance.
Pediatr Cardiol DOI 10.1007/s00246-011-9999-3 Received: 26 February 2011 / Accepted: 7 April 2011
